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A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
metabolism, excluding complex ... MetabolicEmergency #Genetics ... #Diagnosis #Algorithm ... #Differential # ... Pediatrics #Table #IEM
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
of lab values compiled ... See IEM schema for ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... #Table #NICU #Genetics ... #IEM #Laboratory
Hypersensitivity Types and Their Mechanisms
Type I - lgE - Soluble antigen
 - Allergen-specific lgE antibodies bind
II - IgG or IgM ... antigen - IgG or IgM ... Antigen-antibody complexes ... #Classification ... #Pathophysiology
Rapidly Progressive Glomerulonephritis (RPGN) 
 - Loss of kidney function over a short period of tirne
space) Immune-Complex ... autoAb against type ... staining on IF • No EM ... Glomerulonephritis #RPGN #Classification ... #Differential #