94 results
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
schema of the pathophysiology ... inborn errors of metabolism ... connections and pathophysiology ... of information: Pediatrics ... , UpToDate #Pediatrics
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
Inborn Errors of Metabolism ... from UpToDate and Pediatrics ... diagnosing acute metabolic ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... Neonatology #Peds #Pediatrics
Clinical presentation of metabolic or respiratory acidosis.

#acidosis #metabolic #respiratory #picture #diagram #signs #symptoms #presentation #Diagnosis
presentation of metabolic ... or respiratory acidosis ... #acidosis #metabolic ... picture #diagram #signs
Metformin Associated Lactic Acidosis (MALA) 

Pathophysiology of MALA
 - Metformin interferes with the activity of the
Associated Lactic Acidosis ... (MALA) Pathophysiology ... use in cellular metabolism ... acidosis including ... Toxicology #Diagnosis #Management
Tetralogy of Fallot - Hypoxic Spell Management
1. Oxygenation
2. Increase SVR
3. Abolish Hyperpnea
4. Correct Acidosis

- Dr. Rasha
Hypoxic Spell Management ... Correct Acidosis ... Hypoxic #Spell #Management ... #Peds #Pediatrics
Refeeding Syndrome: Pathogenesis and clinical findings

Patients at Risk of Refeeding Syndrome:
 - Little or no nutritional
• Incr Glucose Metabolism ... Syndrome - Metabolic ... Acidosis • Shift ... Syndrome #diagnosis #pathophysiology ... #symptoms #signs
Kussmaul Breathing Pattern

Demonstration of Kussmaul breathing pattern seen here in Diabetic Ketoacidosis.  Initial pH was
associated with severe metabolic ... acidosis. ... Pattern #Pulmonary #Sign
Metabolic Acidosis with Anion Gap - KILU Mnemonic

K - Ketoacidosis
	• DKA
		- With normal glucose, ask if
Metabolic Acidosis ... in lit), iron (pediatric ... Mnemonic #AnionGap #Metabolic ... #Acidosis #diagnosis
Total Anomalous Pulmonary Venous Return (TAPVR)
 • Introduction
 • Classification
 • Pathophysiology of TAPVR
 • Presentation
Classification • Pathophysiology ... Classic “snowman sign ... Pre-Operative Management ... Post-Operative Management ... cardiology #peds #pediatrics
Tetralogy of Fallot Summary
 • Anatomy
 • Incidence
 • Pathophysiology
 • Presentation
 • Common Variants
 •
• Incidence • Pathophysiology ... palliation • Post-Op Management ... Fallot #diagnosis #management ... cardiology #peds #pediatrics