89 results
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
schema of the pathophysiology ... inborn errors of metabolism ... #Pediatrics #Metabolism ... Diagnosis #Algorithm #Differential ... #Neonatology #Peds
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
Inborn Errors of Metabolism ... diagnosing acute metabolic ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... #InbornErrors #Metabolism ... #Neonatology #Peds
Primary Metabolic Alkalosis - Differential Diagnosis Algorithm
Volume Depleted 2° hyperaldosteronism
 • Low Urine Cl-: Vomiting, NGT
Primary Metabolic ... Alkalosis - Differential ... (late) • High Urine ... #Primary #Metabolic ... Diagnosis #Algorithm #nephrology
Primary Metabolic Alkalosis - Differential Diagnosis Algorithm
Volume Depleted - 2° hyperaldosteronism
 • Low Urine Cl-: Vomiting,
Primary Metabolic ... Alkalosis - Differential ... hyperaldosteronism • Low Urine ... (late) • High Urine ... Diagnosis #Algorithm #Nephrology
Metabolic Pathways of Purple Urine Bag Syndrome: Adopted from chart originally published in Purple Urine Bag
Metabolic Pathways ... Bag Syndrome: Adopted ... Bag Syndrome: A ... #Pathophysiology ... #Bag #Syndrome
Purple Urine Bag Syndrome
Chronic, indwelling catheter + bacteriuria (Providencia, Klebsiella, E.coli*) + alkaline urine
Tryptophan → Indoxyl
Purple Urine Bag ... Syndrome Chronic ... #Bag #Syndrome ... #PUBS #pathophysiology ... clinical #photo #differential
Causes of Metabolic Alkalosis - Differential Diagnosis Algorithm
Urine chloride < 20 mmol/l - Chloride responsive (Chloride
Causes of Metabolic ... Alkalosis - Differential ... Diagnosis Algorithm Urine ... diuretic use Urine ... , Gitelman's Syndrome
Causes of Apparent Life Threatening Event (ALTE) - Differential Diagnosis Algorithm
Cardiac:
 • Congenital Heart Disease
 •
Event (ALTE) - Differential ... Myocarditis Metabolic ... • Reye's Syndrome ... Disturbances Neurologic ... Algorithm #Causes #Peds
High Anion Gap Metabolic Acidosis (HAGMA) - Differential Diagnosis - GOLDMARK

Glycols - ethylene and propylene glycol
Oxoproline
High Anion Gap Metabolic ... Acidosis (HAGMA) - Differential ... with short bowel syndrome ... Acidosis #HAGMA #Differential ... GOLDMARK #mnemonic #nephrology
Urine Color - Differential Diagnosis
Red Urine:
 • Medical conditions: bleeding, porphyria, factitious disorder
 • Meds: rifampin,
Urine Color - Differential ... factitious disorder • Meds ... Pseudomonas • Meds ... #Color #Differential ... discoloration #nephrology