61 results
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
Hypersensitivity pneumonitis ... • Radiation pneumonitis ... , Polymyositis-dermatomyositis ... Idiopathic Interstitial Pneumonias ... #diagnosis #differential
ILD of Known Cause - Differential Diagnosis
Exposure:
 • Occupational: Asbestosis, Silicosis, Hypersensitivity, Pneumonitis
 • Treatment Related:
ILD of Known Cause ... - Differential Diagnosis ... Hypersensitivity, Pneumonitis ... Polymyositis, Dermatomyositis ... BrighamChiefs #ILD
Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
DM/PM : dermatomyositis ... ConnectiveTissueDiseases #ILD ... LungDisease #CTILD #Diagnosis ... Table #Pulmonary #Rheumatology
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Seborrhea • Dermatomyositis ... Heliotrope • Dermatomyositis ... gangrenosum • IBD ... #differential #diagnosis ... #rheumatology
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
the disease and ILD ... increases and ILD ... Phenotype 1 ... #rheumatology # ... dermatology #diagnosis
Myositis Specific Antibodies (MSAs)

Dermatomyositis: MDA5, TIF1y, NXP2, Mi-2, SAE
Anti-Synthetase Syndrome: Jo-1, PL7, PL12, EJ, OJ
Immune Mediated
Antibodies (MSAs) Dermatomyositis ... Anti-Synthetase Syndrome: Jo-1, ... MSAs #clinical #diagnosis ... #rheumatology #
Autoimmune Myositis
Necrotizing myopathy is associated with higher CK levels, greater level of muscle weakness, less systemic
Dermatomyositis ... Classic triad of ILD ... /full triad at diagnosis ... Autoimmune #Myositis #diagnosis ... #rheumatology
On the left some diseases with a nodular pattern.
1. Hypersensitivity pneumonitis: ill defined centrilobular nodules.
2. Miliary
nodular pattern. 1. ... Hypersensitivity pneumonitis ... Hypersensitivity pneumonitis ... bronchiolitis: ill ... #Clinical #Diagnosis
Heme Synthesis Pathway
Enzymes
1. ALA Synthase
2. ALA Dehydratase
3. Porphobilinogen deaminase
4. UP Ill Synthase
5. UP Ill Decarboxylase
6. Coproporphyrinogen
Pathway Enzymes 1. ... UP Ill Synthase ... UP Ill Decarboxylase ... Synthesis #Pathway #pathophysiology ... #diagnosis
Dermatomyositis (DM) and Polymyositis (PM): Pathogenesis and clinical findings
Elevated Antinuclear Antibodies: Anti-Jo-1, Anti-OJ, Anti-Mi2, Anti-SRP, Anti-EJ,
Dermatomyositis ... Antibodies: Anti-Jo-1, ... dehydrogenase (LD ... Polymyositis #PM #Diagnosis ... #Pathophysiology