13 results
Hemophilia - Diagnosis and Management
Diagnosis:
 • Consistent bleeding history (unless screening for disease in family members
and Management ... may be normal in mild ... Chronic Management ... Avoid meds that ... #hematology
Clinical Algorithm for Emergency Department Evaluation and Management of UTI in Febrile Infants and Young Children

Urinary
Clinical Algorithm ... Emergency Department Evaluation ... and Management ... UTI #Algorithm #Diagnosis ... #Infant #Peds #
Bronchiolitis - Lower respiratory tract (bronchioles) 

Microbiology 
 • Respiratory syncytial virus (RSV) (most commonl
Influenza virus Clinical ... Respiratory failure Management ... Bronchiolitis #Diagnosis ... #Management #Peds ... #Pediatrics
Croup Diagnosis and Management Pearls
Common childhood illness, usually viral and self limiting. Characterised by a seal-like
Croup Diagnosis ... and Management Pearls ... Evaluation: • Mild ... #Management #pediatrics ... #peds
The 6 C’s of Primary Sclerosing Cholangitis (PSC)
PSC is a chronic, cholestatic, immune-mediated disease characterized by
ducts, commonly leading ... asymptomatic at diagnosis ... remain subject to clinical ... trial evaluation ... #Hepatology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
-1 and IL-6, leading ... Fever is the main clinical ... purpura to mucosal bleeding ... Activation #Syndrome #Diagnosis ... #Management #Hematology
Evaluation of suspected incomplete Kawasaki Disease

1. AHA consensus recommendations
2. Infants ≤6 months old on day ≥7
Evaluation of suspected ... Infants ≤6 months old ... if they have no clinical ... #Diagnosis #Peds ... #Pediatrics #Kawasaki
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
cytokines (TNFa,lL1, IL6 ... accumulation of clinical ... Assessment • Clinical ... inhibitors under evaluation ... #management #treatment
Helpful Clinical Features in Evaluating Bleeding Disorders
Age of onset
 • Neonate - in 20% of haemophilias,
Helpful Clinical ... Features in Evaluating ... #History #peds ... #pediatrics #diagnosis ... #hematology #primarycare
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
to 1:1 F:M • Clinical ... Prognosis: Usually mild ... 40, F:M 9:1 • Clinical ... Usual therapeutic management ... #diagnosis #management