50 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome Systemic ... purpura, Pathergy ... Arthritis, AS Treatment ... #management #signs ... #symptoms #rheumatology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Diagnosis Framework ... CAUSES OF NON-PALPABLE ... PURPURA: Vasculitis ... #Differential #Diagnosis ... #hematology #rheumatology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
central nervous system ... - systemic ... - purpura-arthralgia-nephritis ... #Rheumatology # ... Diagnosis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Symptoms (Sx) in ... scleritis • Palpable ... sign of cutaneous ... Skin -> causing palpable ... #rheumatology #
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Symptoms (SX) in ... sign of cutaneous ... • Progressive symptoms ... ) • Palpable purpura ... #Rheumatology
Henoch Schonlein Purpura 
Typically a young boy. Often occurs following upper respiratory tract infection. A systemic
Henoch Schonlein Purpura ... A systemic vasculitis ... #Diagnosis #Peds ... #Pediatrics #Signs ... #Symptoms
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Butterfly rash, Vasculitis ... , Purpura, Urticaria ... erythematosus #signs ... #symptoms #diagnosis ... #rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
• Petechiae, Palpable ... • Petechiae • Palpable ... Differential Diagnosis ... dermatology #rash #diagnosis ... #rheumatology
Manifestations of IgG4-related disease by organ system.
 The most common primary disease features are indicated in
of IgG4-related disease ... by organ system ... #Organs #Systems ... #Diagnosis #Hematology ... #Signs #Symptoms
Diagnosis of IgA Vasculitis (Henoch-Schönlein Purpura) - French Vasculitis Study Group 

1) Suggestive clinical manifestations
Diagnosis of IgA ... Purpura) - French ... - Symmetric palpable ... disease, skin-dominant ... #Rheumatology #