13 results
Plain radiography of the abdomen revealed calcification of both adrenal glands. A homozygous mutation in LIPA
glands. ... confirmed the diagnosis ... and gut, which causes ... #clincial #peds ... #infant #NEJM #
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
, causes and management ... cryoglobulinemia vasculitis Clinical ... with purpura - Renal ... neuropathy Treatment ... Cryoglobulinemia #Vasculitis #Rheumatology
Staphylococcus-associated GlomeruloNephritis - Diagnosis and Management Summary
CLINICAL
 • Nephritic syndrome (Casts)
 • Marked proteinuria (may be
Staphylococcus-associated ... Management Summary CLINICAL ... Nephritic syndrome (Casts ... • Vasculitic rash ... deposits common TREATMENT
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Related Disease Clinical ... pancreas, biliary, renal ... aorta, salivary glands ... supporting long-term ... #rheumatology
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
(blue-purple) rash ... Violaceous papules or plaques ... auricular papules Clinical ... Dermatomyositis #rheumatology ... #dermatology #diagnosis
Lichen Planus- ...On examination, numerous purple papules were noted on the anterior surface of the forearms
sawtooth rete pegs ... confirming the diagnosis ... used in primary treatment ... #NEJM #clinical ... #derm #wickhams
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... tract, and often causes ... glomerulonephritis) • Anti-GBM ... mucositis - Rash ... #rheumatology #
Posterior Reversible Encephalopathy Syndrome (PRES) Overview

Clinico-Radiological Syndrome, characterized by:
 • Headache
 • Seizures
 • Altered mental
fluctuations PRES-Associated ... epilepticus Treatment ... the underlying cause ... • Treatment of ... until cause identified
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
salivary and lacrimal glands ... Primary form: not associated ... salivary ducts Clinical ... Adenocarcinoma Treatment ... Sjogrens #Syndrome #Rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
pulmonary and renal ... , mucositis • Rash ... VASCULITIS: ANCA Associated ... tract, and often causes ... #Rheumatology