11 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... Behcet syndrome (Clinical ... ) Differential Diagnosis ... Giant retinal tears ... Syndrome #diagnosis #management
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Clinical triad ... Fever, Arthralgia/arthritis ... fraction < 20% Differential ... #diagnosis #management
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Somatic) Syndrome Clinical ... Features: alveolitis, ear ... thromboembolic disease ... • giant cell arteritis ... myeloid cells NEJM
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
Diagnosis = clinical ... very remarkable w/differential ... in literature (NEJM ... cases (Cornelia NEJM ... Symptoms #Diagnosis #Management
Myasthenic Crisis Checklist - Myasthenia Gravis

Evaluation 
 - Chest X-ray and lung ultrasound (exclude other lung
Myasthenic Crisis Checklist ... Phos), CBC with differential ... Intubation only if clinically ... (vital signs, clinical ... #Management #CriticalCare
Peripartum Cardiomyopathy - Summary
1. Definition
 • Towards the end of pregnancy to 5 months postpartum
Differential Diagnosis ... Valvular heart disease ... Congenital heart disease ... Clinical • Under-recognized ... with Cardio-OB team
Transverse Myelitis Overview

Focal inflammatory disorder of the spinal cord resulting in rapid onset of weakness, sensory
super-antigen mediated disease ... Transverse Myelitis - Clinical ... MCTD - Bechet disease ... Myelitis #diagnosis #management ... #neurology #differential
Polymyalgia Rheumatica (PMR) Diagnosis and Management Summary

WHAT?
 • Polymyalgia rheumatica (PMR) is a common systemic inflammatory
Diagnosis and Management ... CLINICAL: • Physical ... for giant cell arteritis ... diagnosed based on clinical ... normal and can help differentiate
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
multisystemic disease ... salivary ducts Clinical ... Arthralgia and Arthritis ... Symptomatic: artificial tears ... Rheumatology #Diagnosis #Management
Condylomata lata in Secondary Syphilis
Condylomata lata lesions usually present as gray, raised papules that sometimes appear
the vulva or near ... condylomata acuminata, a differential ... resemble other disease ... Secondary #Syphilis #Clinical ... #Photo