13 results
Causes of Portal Hypertension According to Site of Vascular Obstruction
1) Prehepatic pre-sinusoidal: Portal vein thrombosis due
Site of Vascular Obstruction ... to cirrhosis, Abdominal ... , Nodular regenerative ... Veno-occlusive disease ... post-sinusoidal: Budd-Chiari syndrome
Portal Hypertension Classification by site of vascular obstruction
1) Post-hepatic Post-sinusoidal: Budd-Chiari syndrome
2) Intrahepatic Post-sinusoidal: Veno-occlusive disease
3)
site of vascular obstruction ... Post-sinusoidal: Budd-Chiari syndrome ... Veno-occlusive disease ... , Nodular regenerative ... to cirrhosis, Abdominal
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... Giant retinal tears ... Leukemia, Lymphoma Ocular ... • Nonsurgical abdominal ... signs #symptoms #rheumatology
Chronic Abdominal Pain Causes - Differential Diagnosis Framework

Many patients with chronic abdominal pain have had prior
• Budd-Chiari syndrome ... • Intestinal obstruction ... Irritable bowel syndrome ... Hypothyroidism • Lead ... artery compression syndrome
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Glomerulonephritis, arthritis, obstructive ... - GI tract: abdominal ... well as inner ear ... Supply gut -> abdominal ... differential #diagnosis #rheumatology
Iron Deficiency Anemia - Differential Diagnosis Algorithm

Labs: Ferritin, iron, transferrin, TIBC, TSAT, sTfR

 • Blood loss:
Gastrectomy, WHDA syndrome ... Structural: Celiac disease ... Copper deficiency, Lead ... diet, Alcoholism, Tea-toast ... Algorithm #ferritin #hematology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
multiplex • GI tract: Abdominal ... gut involvement, abdominal ... Glomerulonephritis, arthritis, obstructive ... : Ocular inflammatory ... Differential #Diagnosis #Rheumatology
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
- Capillary leak ... , paresthesia, abdominal ... month at least 1 year ... #Capillary #leak ... timeline #treatment #rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
of 37°C to the near-freezing ... pulmonary emboli, and ocular ... Antiphospholipid syndrome ... Cryofibrinogenemia #diagnosis #rheumatology ... #hematology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• Heavy Chain disease ... Systemic capillary leak ... Hypergammaglobulinemic macular ... Sneddon-Wilkinson disease ... Paraproteinemias #Hematology