9 results
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Glomerulonephritis, arthritis, obstructive ... - GI tract: abdominal ... well as inner ear ... Supply gut -> abdominal ... differential #diagnosis #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... ulceration • Ocular ... Giant retinal tears ... • Nonsurgical abdominal ... signs #symptoms #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
multiplex • GI tract: Abdominal ... gut involvement, abdominal ... Glomerulonephritis, arthritis, obstructive ... • Cogan syndrome ... Differential #Diagnosis #Rheumatology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
Systemic capillary leak ... Autoimmunity: • -MM/WM: Vasculitis ... Hypergammaglobulinemic macular ... Vasculitis) Autoantibodies ... Paraproteinemias #Hematology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
of 37°C to the near-freezing ... malignancies, vasculitis ... pulmonary emboli, and ocular ... Antiphospholipid syndrome ... Cryofibrinogenemia #diagnosis #rheumatology
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
Disease - Capillary leak ... , paresthesia, abdominal ... month at least 1 year ... Disease #Capillary #leak ... timeline #treatment #rheumatology
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
gland) biopsy • Ocular ... ) • Cutaneous vasculitis ... : 2% Systemic Vasculitis ... Symptomatic: artificial tears ... #Rheumatology #
Cystic Duct Stone on Biliary POCUS

Not your average gall stone. This stone is lodged in the
Stone on Biliary POCUS ... duct stones can lead ... to Mirizzi syndrome ... common hepatic duct obstruction ... #ultrasound #abdominal
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
chondritis • Ocular ... Eyes • Inner ear ... like "cauliflower ear ... Airway collapse or obstruction ... Polychondritis #rheumatology