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Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... skin injury) • Neurologic ... and diplopia) • Vascular ... spondyloarthritis • Ocular ... Leukemia, Lymphoma Ocular
Rheumatoid Arthritis - Signs and Symptoms
 • Ocular: Keratoconjunctivitis sicca, Episcleritis, Scleritis, Scleromalacia perforans
 • Pulmonary:
Ocular: Keratoconjunctivitis ... Rheumatoid nodules, Vascular ... Mononeuritis multiplex • Vascular ... : Rheumatoid vasculitis ... Atherosclerosis • Cardiac: Coronary
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
purpura: Strong sign ... pulse deficits vascular ... pulmonary disease, and ocular ... ulcers, cutaneous, ocular ... Cogan syndrome: Ocular
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
pulmonary disease, and ocular ... ulcers, cutaneous, ocular ... aneurysms can also ... Syndrome: - Ocular ... purpura: strong sign
Amyotrophic Lateral Sclerosis (ALS) Summary
ALS: combination of the clinical examination finding of amyotrophy with the pathologic
of UMN and LMN signs ... 4) progressive muscular ... fasciculations Common Symptoms ... EMG: LMN Signs in ... Lateral #Sclerosis #neurology
Causes of Secondary Hypertension - Workup and Differential Diagnosis
Approach (when evaluation should be done):
1. Severe or
hypertension and signs ... renal bruit or signs ... Causes: • Vascular ... Coarctation of aorta, Vasculitis ... Neurologic disorders
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
cryoglobulin (CG ... Cryofibrinogenemia Symptoms ... Hyperviscosity, - Vascular ... malignancies, vasculitis ... pulmonary emboli, and ocular
PALM RASHES 
Common features and patterns:
1.	Color:
o	Red or erythematous: Common in inflammatory or allergic reactions.
o	Purple or purpuric:
purpuric: May suggest vascular ... inflammation (vasculitis ... Texture: o Flat (macular ... 5 Associated Symptoms ... infection, or vascular