206 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... more): Genital ulceration ... Behcet syndrome (Clinical ... diagnosis #management #signs ... #symptoms #rheumatology
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
complicated of ulcerations ... • Skin ulcerations ... auricular papules Clinical ... severity of the disease ... Dermatomyositis #rheumatology
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
chest (in a V-sign ... • Skin ulcerations ... auricular papules Clinical ... had more severe disease ... diagnosis #management #rheumatology
Cutaneous and Systemic Findings in Dermatomyositis
Cutaneous Findings:
 - Heliotrope sign and edema
 - Nail-fold changes
 -
- Heliotrope sign ... or shawl sign ... Interstitial lung disease ... tract - Cardiac disease ... Dermatomyositis #Diagnosis #Rheumatology
Clinical Manifestations of Systemic Lupus Erythematosus (SLE)

#Systemic #Lupus #Erythematosus #SLE #Manifestations #Signs #Symptoms #Rheumatology #Diagnosis
Clinical Manifestations ... Manifestations #Signs ... #Symptoms #Rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
GPA causes disease ... Rarely dominate the clinical ... Oral and nasal ulcerations ... Bullae/Blisters • Ulceration ... rash #diagnosis #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Hemorrhagic bullae, Ulceration ... racemosa, Digital ulceration ... Vasculitis: • Behcet Disease ... #dermatology #rheumatology
Polycystic Kidney Disease - Clinical Signs and Symptoms

#ADPKD #Polycystic #Kidney #Disease #Signs #Symptoms #Diagnosis
Polycystic Kidney Disease ... - Clinical Signs ... Polycystic #Kidney #Disease ... #Signs #Symptoms
Manifestations of IgG4-related disease by organ system.
 The most common primary disease features are indicated in
of IgG4-related disease ... common primary disease ... Manifestations #Disease ... Systems #Diagnosis #Hematology ... #Signs #Symptoms
Pyoderma Gangrenosum: Autoimmune disorder resulting in a vasculitis which causes slowly progressive 
ulceration of the skin.
progressive ulceration ... number of systemic diseases ... inflammatory bowel disease ... UCSD Catalog of Clinical ... Images #Clinical