543 results
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Dermatologic Manifestations ... Oral and nasal ulcerations ... Bullae/Blisters • Ulceration ... vasculitis #Dermatologic ... rash #diagnosis #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Hemorrhagic bullae, Ulceration ... racemosa, Digital ulceration ... Vasculitis: • Behcet Disease ... Vasculitis #skin #dermatology ... #rheumatology #
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
complicated of ulcerations ... • Skin ulcerations ... severity of the disease ... Dermatomyositis #rheumatology ... #dermatology #diagnosis
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
complicated of ulcerations ... • Skin ulcerations ... had more severe disease ... diagnosis #management #rheumatology ... #dermatology
Mucous Membrane Disorder - Differential Diagnosis Algorithm
Erosions/Ulcers/Blisters
 - Primary Dermatologic Diseases
     •
Blisters - Primary Dermatologic ... Diseases ... (ulcerative colitis ... more than Crohn's disease ... MucousMembranes #dermatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Manifestations: • Oral Ulcerations ... oral aphthous ulcerations ... more): Genital ulceration ... , ulcerative colitis ... signs #symptoms #rheumatology
Diagnostic Schema for Hyperferritinemia

Pearl: Diseases associated with extreme elevations: 
1. HLH 
2. Still's disease 
3. Systemic
Hyperferritinemia Pearl: Diseases ... Still's disease ... Differential #Diagnosis #Hematology
Mayo UC Endoscopic Classification
 • Score = 0 (normal or inactive disease) - Normal vascular pattern
normal or inactive disease ... Score = 1 (mild disease ... = 2 (moderate disease ... Spontaneous bleeding, ulcerations ... Classification #ulcerative
Ulcerative Colitis - Endoscopic Assessment of Disease Activity
UCEIS Score 0, Mayo Score 0 - Normal
UCEIS Score
Ulcerative Colitis ... Assessment of Disease ... Spontaneous bleeding, ulceration ... #Ulcerative #Colitis
Pyoderma Gangrenosum: Autoimmune disorder resulting in a vasculitis which causes slowly progressive 
ulceration of the skin.
progressive ulceration ... number of systemic diseases ... inflammatory bowel disease ... suffers from Crohn's Disease ... Clinical #Photo #Dermatology