158 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... oral aphthous ulcerations ... more): Genital ulceration ... Behcet syndrome (Clinical ... signs #symptoms #rheumatology
Causes of Nail Clubbing - Mnemonic 
Cyanotic Heart Disease, Cystic Fibrosis
Lung Cancer, Lung abscess 
Ulcerative Colitis
Cyanotic Heart Disease ... Lung abscess Ulcerative ... Endocarditis, Idiopathic Pulmonary ... Gastrointestinal Disease
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
GPA causes disease ... Rarely dominate the clinical ... Oral and nasal ulcerations ... Bullae/Blisters • Ulceration ... rash #diagnosis #rheumatology
Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
Connective tissue disease-associated ... interstitial lung diseases ... connective tissue disease ... Comparison #Table #Pulmonary ... #Rheumatology #
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Hemorrhagic bullae, Ulceration ... racemosa, Digital ulceration ... Vasculitis: • Behcet Disease ... #dermatology #rheumatology
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Clinical triad ... autoinflammatory diseases ... hepatitis • Pulmonary ... management #treatment #rheumatology
Pyoderma Gangrenosum: Autoimmune disorder resulting in a vasculitis which causes slowly progressive 
ulceration of the skin.
progressive ulceration ... number of systemic diseases ... inflammatory bowel disease ... UCSD Catalog of Clinical ... Images #Clinical
Raynaud's Phenomenon on Physical Exam

#Raynauds #Syndrome #disease #phenomenon #clinical #video #physicalexam #fingers #hands #rheumatology
Raynauds #Syndrome #disease ... #phenomenon #clinical ... fingers #hands #rheumatology
Systemic Sclerosis Associated Autoantibodies
Anti-topoisomerase I (anti-Sc170): Diffuse skin disease, Pulmonary fibrosis
Anti-centromere: Limited skin disease (~93-95%), Pulmonary
: Diffuse skin disease ... , Pulmonary fibrosis ... : Limited skin disease ... (~93-95%), Pulmonary ... Autoantibodies #diagnosis #rheumatology
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... due to lung disease ... lung disease Other ... pulmonary disease ... , Gaucher disease