27 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... medium-large joints) • Vascular ... : Ocular Behcet's ... and peripheral vascular ... Diagnosis #criteria #rheumatology
Behcet's Syndrome - Treatment
Ulcers:
 • Treatment: Topical steroids
 • Prevention: Colchicine
 • Azathioprine for refractory disease
Arthritis:
Behcet's Syndrome ... refractory lesions Ocular ... immunosuppressive meds) Vascular ... #disease #Syndrome ... #pharmacology #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome ... ulceration • Ocular ... and diplopia) • Vascular ... Leukemia, Lymphoma Ocular ... signs #symptoms #rheumatology
Uveitis - Definition, Causes and SUN Classification

Inflammation of the iris, ciliary body, vitreous, retina and/or choroid
Incidence
blindness, linked to macular ... , sarcoidosis, Behcet ... Ophthalmology #Rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
IgM deposits • Nodular ... Vasculitis: • Behcet ... Disease • Cogan syndrome ... #dermatology #rheumatology
Opsoclonus-Myoclonus Ataxia Syndrome (OMAS) -Dancing eyes - dancing feet syndrome
 • Opsoclonus: ocular spontaneous, arrhythmic, conjugate
Opsoclonus-Myoclonus Ataxia Syndrome ... - dancing feet syndrome ... • Opsoclonus: ocular ... movements caused by muscular ... #clinical #video
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
capillary leak syndrome ... Hyperviscosity syndrome ... Hypergammaglobulinemic macular ... (Thrombosis in vascular ... Paraproteinemias #Hematology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
and bullous or vesicular ... VASCULITIS: • Behçet ... Syndrome: - Recurrent ... • Cogan Syndrome ... differential #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
pulse deficits vascular ... vasculitis • Behcet ... syndrome: Recurrent ... : Ocular inflammatory ... Differential #Diagnosis #Rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Hyperviscosity, - Vascular ... pulmonary emboli, and ocular ... Antiphospholipid syndrome ... Cryofibrinogenemia #diagnosis #rheumatology ... #hematology