32 results
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Non-hepatitis C virus Cryoglobulinemia ... MONOCLONAL CRYOGLOBULINEMIA ... lenalinomide MIXED CRYOGLOBULINEMIA ... TerrierBen #NonHCV #Cryoglobulinemia ... Monoclonal #Mixed #Cryoglobulinemic
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Diagnosis of Cryoglobulinemia ... ) MONOCLONAL CRYOGLOBULINEMIA ... syndrome MIXED CRYOGLOBULINEMIA ... TerrierBen #Cryoglobulinemia ... #Rheumatology #Cryoglobulinemic
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
infectious mixed cryoglobulinemia ... < 5% of mixed cryoglobulinemia ... TerrierBen #NonHCV #Cryoglobulinemia ... Rheumatology #Mixed #Cryoglobulinemic
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
in 35% of mixed cryoglobulinemia ... neuropathy • Type II cryoglobulinemia ... #Involvement #Cryoglobulinemia ... #Rheumatology #Cryoglobulinemic
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Cryoglobulinemia ... Mainly in Type I Cryoglobulinemia ... Triad - Mixed Cryoglobulinemia ... with the mixed cryoglobulinemia ... Etiology - Mixed Cryoglobulinemia
Cryoglobulinemia Classification Types

Type 1: Monoclonal IgM (rarely IgG/lgA)
 • Raynaud phenomenon, Digital ulcers/gangrene, Livedo reticularis, Hyperviscosity
Cryoglobulinemia ... MatthewHoMD #Cryoglobulinemia
Cryoglobulinemia Vasculitis
#rheumatology #diagnosis #signs
Cryoglobulinemia
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
deposits: Type I cryoglobulinemia ... activity: Type II cryoglobulinemia
Glomerulonephritis - Differential Diagnosis Framework
ANCA:
 • C-ANCA: GPA (Wegener's)
 • P-ANCA: Microscopic Polyangiitis, Eosinophilic GPA (Churg
• ↓C4: Lupus, Cryoglobulinemia
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
POEMS, AL amyloid, Cryoglobulinemia ... Schnitzler syndrome • Cryoglobulinemia