Mithu Maheswaranathan, MD @MithuRheum
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Rheumatologist at Duke University Creator of Rheum OnePagers ➡ RheumOnePagers.com Twitter: @MithuRheum ➡ https://twitter.com/MithuRheum
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Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
• Giant Cell Arteritis ... (GCA) • Takayasu's ... arteritis (TAK) ... • Polyarteritis ... ACR2021 #Guidelines #algorithm
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
VEXAS (Vacuoles, E1 ... Syndrome (32%) • polyarteritis ... • giant cell arteritis ... • UBA1 = major E1 ... Syndrome #Vacuoles #E1
Giant Cell Arteritis (GCA) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Visual Symptoms/Loss or
Giant Cell Arteritis ... (GCA) - Vasculitis ... Management Algorithm ... MithuRheum #GiantCell #Arteritis ... ACR2021 #Guidelines #algorithm
Aortitis - Differential Diagnosis Framework
Non-Infectious Aortitis:
 • Vasculitides: Giant Cell Arteritis (GCA), Takayasu's arteritis, Cogan's Syndrome,
Vasculitides: Giant Cell Arteritis ... (GCA), Takayasu's ... arteritis, Cogan's ... Behcet's Disease, Polyarteritis ... RD), Rheumatoid Arthritis
Polyarteritis Nodosa (PAN) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Severe Disease → Remission
Polyarteritis Nodosa ... Vasculitis Management Algorithm ... with CYC over GC ... MithuRheum #PAN #Polyarteritis ... ACR2021 #Guidelines #algorithm
Takayasu's Arteritis (TAK) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active TAK not on
Takayasu's Arteritis ... Vasculitis Management Algorithm ... High-dose daily oral GC ... TAK #Takayasus #Arteritis ... ACR2021 #Guidelines #algorithm