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Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
• Heavy-chain (AH ... in AA and AL Cardiac ... Bone/Joint: • Amyloid ... (AMYLOID ANGIOPATHY ... typing Cardiac
Cardiac Amyloidosis Management
The liver produces transthyretin tetramers, which dissociate into monomers and mis-fold, then aggregate into
Cardiac Amyloidosis ... aggregate into amyloid ... fibrils and deposit ... into cardiac tissue ... Cardiac amyloidosis