2 results
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Group of disorders ... • Heavy-chain (AH ... Clinical suspicion ... Clinical Manifestations ... : • Nephrotic syndrome
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
Clinical Presentation ... Diagnostic Criteria ... of 8 HLH-2004 criteria ... malignancy, autoimmune disorder ... Diagnosis #Management #Hematology