8 results
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Rapidly Progressive ... Post-strep GN, Lupus ... With associated pulmonary ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... Diagnosis Framework Diffuse ... hemorrhage + rapidly progressive ... anti-GBM) 10%: - Low Complement ... - Normal Complement
Causes of Hemoptysis - Differential Diagnosis Algorithm
Massive Hemoptysis (>I00 mL in 24 hours)
 • Malignancy
 •
Differential Diagnosis Algorithm ... • Bronchitis Diffuse ... Vasculitis Infection ... Vasculitis • ... Lupus Erythematosus
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Definition: Diffuse ... ANCA-positive vasculitis ... ANCA-negative vasculitis ... Complex: Systemic lupus ... anti-CCP • CXR (diffuse
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
proteinuria, rapidly progressing ... GN • New pulmonary ... inflammation Others: • Lupus ... such as systemic lupus ... against MPO • Complement
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
anti-Smith Ab, low complements ... ANCA-associated vasculitis ... pneumonitis • Diffuse ... enteropathy, and diffuse ... RNP antibodies, Complement
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... palpable purpura 2/2 vasculitis ... capillaritis leading to diffuse ... hemorrhage (DAH) • Diffuse ... Path: rapidly progressive
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Differential Diagnosis Algorithm ... Pneumonia - slowly progressive ... leaking out of pulmonary ... Arthritis, Systemic Lupus ... Differential #Diagnosis #Algorithm