18 results
Complete AV Canal Defect on Echocardiogram

Among pts with Pulmonary Arterial Hypertension, those with Eisenmenger syndrome have
Complete AV Canal ... Defect on Echocardiogram ... Complete AV canal ... Ivan_Echocardio #CAVCD ... #Complete #AVCanal
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Causes of Purpura - Differential Diagnosis
Non-PalpabIe → Palpable
 • Thrombocytopenia (HIT, ITP/HUS), Coagulation defects (DIC, warfarin
Causes of Purpura ... Leukocytoclastic Vasculitis ... (LCV), Immune complex ... nonpalpable #palpable #Causes ... Differential #Diagnosis #vasculitis
Causes of Seizures - Differential Diagnosis Algorithm
Unprovoked - Epilepsy:
 • Focal: Simple, Complex
 • Generalized: Absence,
Causes of Seizures ... Focal: Simple, Complex ... malformation, Aneurysm, Vasculitis ... Diagnosis #Algorithm #Causes
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
pathophysiologic causes ... immunofluorescence Immune Complex ... Glomerulonephritis #Vasculitis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... When to Consider Vasculitis ... tracts Immune Complex ... Vasculitis • ... tract, and often causes
IgA Vasculitis – Henoch Scholein Purpura: Pathogenesis and Clinical Findings

 - Infectious Agents - 50% have
IgA Vasculitis – ... adhesion of IgA complexes ... Formation of immune complexes ... periumbilical region), nausea ... #HSP #IgA #Vasculitis
Causes of Petechial Rash - Differential Diagnosis Algorithm

Pinpoint areas (less than 2 mm) of hemorrhage, which
Causes of Petechial ... Infection - Vasculitis ... - Autoimmune Vasculitis ... Work Up: • Complete ... Diagnosis #Algorithm #Causes
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
deposit of immune complexes ... • They can cause ... Cryoglobulins Cause ... • IgA vasculitis ... • Vasculitis
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
precipitation of a complex ... precipitating complex ... cold insoluble complex ... malignancies, vasculitis ... cryoglobulins • Negative causes
Polyarteritis Nodosa (PAN): Pathogenesis and Clinical Findings

Medical Comorbidities Malignancies (most commonly hairy-cell leukemia)
Immunogenetic Predisposition: patient is
antigen-antibody complexes ... Viral replication causes ... Signs #Symptoms #Vasculitis