59 results
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology ... antibiody -> Immune Complex ... > Incr Immune Complex ... Formation -> Vasculitis ... #HUV #Pathophysiology
Complete AV Canal Defect on Echocardiogram

Among pts with Pulmonary Arterial Hypertension, those with Eisenmenger syndrome have
Complete AV Canal ... with Eisenmenger syndrome ... Complete AV canal ... Ivan_Echocardio #CAVCD ... #Complete #AVCanal
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Causes of Seizures - Differential Diagnosis Algorithm
Unprovoked - Epilepsy:
 • Focal: Simple, Complex
 • Generalized: Absence,
Causes of Seizures ... Focal: Simple, Complex ... malformation, Aneurysm, Vasculitis ... vasoconstriction syndrome ... Diagnosis #Algorithm #Causes
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Churg-Strauss syndrome ... - Immune-complex-induced ... - Goodpasture syndrome ... - Schnitzler syndrome ... - Sjögren syndrome
Acute Spinal Cord Injuries: Pathogenesis and clinical findings
 • Anterior Cord Syndrome -> Anterior spinal artery
Anterior Cord Syndrome ... vascular event -> Complete ... > Often mimics complete ... -> Complete hemicord ... #diagnosis #pathophysiology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... : • Immune Complex ... Vasculitis: - ... Disease • Cogan syndrome
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal Syndrome ... ANCA-positive vasculitis ... ANCA-negative vasculitis ... IgA-associated vasculitis ... Cryoglobulinemia) • Immune Complex
IgA Vasculitis – Henoch Scholein Purpura: Pathogenesis and Clinical Findings

 - Infectious Agents - 50% have
adhesion of IgA complexes ... Formation of immune complexes ... periumbilical region), nausea ... nephrotic/nephritic syndrome ... HenochScholeinPurpura #Pathophysiology
Mechanical Bowel Obstruction and Ileus - Pathogenesis and Clinical Findings
Ileus: Functional bowel "blockage", no peristalsis
Mechanical Obstruction:
of bowel lumen Complete ... bowel-movements (suggests complete ... light-switch pain") with complete ... percussion • Nausea ... obstruction #sbo #ileus #pathophysiology
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
three primary pathophysiologic ... causes differentiated ... immunofluorescence Immune Complex ... Glomerulonephritis #Vasculitis