40 results
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Differential Diaqnoses ... abnormalities • Muscular ... #diagnosis #management ... #treatment #rheumatology
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
Multi-system autoimmune disease ... myositis overlap • Vascular ... Scleroderma #SSc #rheumatology ... #diagnosis #signs ... #symptoms #testing
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... Retroperitoneum and aorta ... IgG4 #Related #Disease ... #diagnosis #management ... workup #treatment #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
meningitis), MCC CNS symptoms ... and diplopia) • Vascular ... ) Differential Diagnosis ... #management #signs ... #symptoms #rheumatology
Hansen's Disease (Leprosy)
 • Transmission - not completely understood, ?nasal droplets
 • Symptoms appear ~5 years
Hansen's Disease ... nasal droplets • Symptoms ... Macrophages with a vacuolar ... #Leprosy #diagnosis ... #management #treatment
COVID-19 - A Seattle Intensivist's One-Page Cheat-Sheet on COVID-19 v2.7 Updated March 26 2020

(v2.7) incorporating newer
more details and clarified ... Infection: Coronavirus Disease ... emergency 2020-3-12 Diagnosis ... unilateral* • POCUS ... #Management #Summary
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Cryofibrinogenemia Symptoms ... Hyperviscosity, - Vascular ... Cryofibrinogenemia Diagnosis ... Cryofibrinogenemia #diagnosis ... #rheumatology #
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
and bullous or vesicular ... < 30 years - Aorta ... branches • GCA: - Aorta ... Presentation - Systemic Symptoms ... #rheumatology #
Aortic Dissection Pearls
Aortic dissection is caused by a tear in the tunica intima, the innermost layer
the wall of the aorta ... • Aortic valve disease ... Aortic #Dissection #diagnosis ... #management #vascular
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
< 30 years • Aorta ... pulse deficits vascular ... Arteritis): • Aorta ... • Progressive symptoms ... #Rheumatology