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Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
lung diseases LIP ... I-JIP: usual interstitial ... AIP: acute interstitial ... ConnectiveTissueDiseases #ILD ... #Comparison #Table
The fourth pattern includes abnormalities that result in decreased lung attenuation or air-filled lesions.
These include:
- Emphysema
-
Lung cysts (LAM, LIP ... #Diagnosis #Radiology ... #Pulmonary #CTChest ... LowAttenuation #Differential ... #Diagram #Comparison
Upper lung zone preference is seen in:
- Inhaled particles: pneumoconiosis (silica or coal)
- Smoking related diseases
(centrilobular emphysema ... bronchiolitis (RB-ILD ... is seen in: - UIP ... edema #Diagnosis #Radiology ... HRCT #ChestCT #Differential
UIP with honeycombing (left) and chronic HP (right)
Differential diagnosis of Hypersensitivity Pneumonitis.
Subacute stage:
- RB-ILD: seen in
UIP with honeycombing ... Subacute stage: - RB-ILD ... Chronic stage: - UIP ... #CTChest #UIP # ... Fibrosis #Mimic #ILD
The idiopathic interstitial pneumonias (IIPs) comprise a heterogenous group of disorders. 
They represent fundamental responses of
findings of NSIP, UIP ... , OP and LIP have ... #Diagnosis #Radiology ... #Pulmonary #CTChest ... IdiopathicInterstitialPneumonia #ILD
Differential diagnosis of Langerhans cell histiocytosis.
Nodular LCH:
- Sarcoidosis: perilymphatic distribution.
- Metastases: random distribution.
Cystic LCH:
- LAM: round
Centrilobular emphysema ... central dot. - LIP ... Clinical #Diagnosis #Radiology ... #CTChest #Cystic ... #Comparison #Table
Cavities frequently arise within a mass or an area of consolidation as a result of necrosis.
We
can heal and end up ... usually contain air ... Clinical #Diagnosis #Radiology ... #CTChest #Cavity ... #Comparison #RadiologyAssistant
Acute interstitial pneumonia (AIP, earlier named Hamman Rich Pneumonitis) is a rare idiopathic lung disease characterized
(AIP, earlier named ... HRCT findings in AIP ... the diagnosis AIP ... #CTChest #AIP # ... AcuteInterstitialPneumonia #ILD
On the left a smoker with RB-ILD with subtle HRCT-findings.
The dominant pattern is ground glass opacification.
Additional
smoker with RB-ILD ... are paraseptal emphysema ... first think RB-ILD ... #CTChest #RBILD ... RespiratoryBronchiolitis #ILD