18 results
Acquired von Willebrand Syndrome - Diagnosis and Management
 • Autoantibodies to vWF: Lymphoproliferative disorders (e.g. lymphoma,
von Willebrand Syndrome ... Diagnosis and Management ... Lymphoproliferative disorders (e.g ... Myeloproliferative disorders (e.g ... #treatment #hematology
Consensus Indications for Irradiated RBC Transfusions:

Cellular blood components are irradiated for the prevention of TA-GVHD. Transfused
disorders (DiGeorge Syndrome ... antithymocyte globulin, etc ... HLA-selected products (e.g ... #Indications #Hematology ... #BloodBank #Management
Clubbing of the Fiingers: Bulbous appearance of the distal fingers associated with a 
number of uncommon
lung conditions (e.g ... , IPF, cancer, etc ... Images #Clinical ... #Photo #Clubbing ... #Fingernails #UCSDH
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Clinical Presentation ... underlying disease (eg ... • Infection (eg ... #Diagnosis #Management ... #Hematology #Rheumatology
Leukostasis vs Tumor Lysis Syndrome
Leukostasis:
 • Pathophysiology: Large, immature blasts and high WBC count cause hyperviscosity
vs Tumor Lysis Syndrome ... hyperviscosity syndrome ... unless worrisome EKG ... TLS #diagnosis #management ... #hematology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
antiinflammatory properties e.g ... Tetracyclines etc ... #Rheumatology # ... diagnosis #management ... #Dermatology
Stiff Person Syndrome (SPS) - Diagnosis and Management Summary

Epidemiology:
 • Prevalence: 1-2 cases per million -
Diagnosis and Management ... Clinical Manifestations ... unit activity on EMG ... of diazepam • EMG ... EMG Studies:
CNS Manifestations of Systemic Lupus Erythematosus (SLE)

Clinical Manifestations: Demyelinating Syndrome, Headache, Movement disorders, Seizure disorders, Aseptic
Erythematosus (SLE) Clinical ... Demyelinating Syndrome ... Lumbar Puncture, EEG ... CNS #neurology #rheumatology ... cerebritis #diagnosis #management
Clubbing of the Fiingers: Bulbous appearance of the distal fingers associated with a number of uncommon
lung conditions (e.g ... IPF, cancer, etc ... Images #Clinical ... #Photo #Clubbing ... #Fingernails #SchamrothsSign
Statin Induced Muscle Toxicity - Summary

Clinical Presentation:
 • Elevations of serum creatine kinase with proximal myalgia
Toxicity - Summary Clinical ... polymyositis, dermatomyositis ... IU/I • SAMS clinical ... (SAMS-CI) • EMG ... myopathy #diagnosis #management