17 results
Acquired von Willebrand Syndrome - Diagnosis and Management
 • Autoantibodies to vWF: Lymphoproliferative disorders (e.g. lymphoma,
von Willebrand Syndrome ... - Diagnosis and ... Management • ... #Diagnosis #Management ... #treatment #hematology
Congenital Long QT Syndrome: Illness Script

Who?
 - Kids or young adults, usually < 30
 - high
Syndrome: Illness ... **Get baseline EKG ... abnormalities - Avoid QTc ... post-arrest or very long QTc ... #Diagnosis #Cardiology
Consensus Indications for Irradiated RBC Transfusions:

Cellular blood components are irradiated for the prevention of TA-GVHD. Transfused
immunodeficiency disorders ... (DiGeorge Syndrome ... HLA-selected products (e.g ... #Indications #Hematology ... #BloodBank #Management
CNS Manifestations of Systemic Lupus Erythematosus (SLE)

Clinical Manifestations: Demyelinating Syndrome, Headache, Movement disorders, Seizure disorders, Aseptic
Demyelinating Syndrome ... Headache, Movement disorders ... , Seizure disorders ... Lumbar Puncture, EEG ... #management #treatment
Stiff Person Syndrome (SPS) - Diagnosis and Management Summary

Epidemiology:
 • Prevalence: 1-2 cases per million -
and Management ... other neurological disorders ... antibody that works ... limb or joint disorders ... #Management #treatment
Vasospastic (Prinzmetal) Angina
Definition / Epidemiology:
 • Rest angina attributed to coronary artery vasospasm.
 • Patients often
other vasospastic disorders ... Raynaud, migraine, etc ... changes on tele/ECG ... Prinzmetal #Angina #cardiology ... #diagnosis #management
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
chronic inflammatory disorder ... Autoinflammatory disorder ... antiinflammatory properties e.g ... Tetracyclines etc ... diagnosis #management
WOBBLER  for ECG assessment in Syncope 
W - Wolff Parkinson White 
O - Obstructed AV
WOBBLER for ECG ... cardiomyopathy, a rare disorder ... syndrome too ... #ECG #Diagnosis ... #Cardiology
Weakness - Differential Diagnosis Framework

Approach To Weakness:
 • Non-neuromuscular disorder (Cardiac, pulmonary etc)
 • CNS ->
- Differential Diagnosis ... Non-neuromuscular disorder ... Cardiac, pulmonary etc ... • Inflammatory disorders ... dystrophies Work
Hypertensive Disorders of Pregnancy
Chronic Hypertension:
 • Guidelines as SBP ≥130 or DBP ≥ 90 mmHg
 •
Hypertensive Disorders ... And Proteinuria (e.g ... patients • HELLP: Syndrome ... #Hypertensive #Disorders ... htn #obstetrics #cardiology