14 results
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... pathologically or clinically ... StanfordChiefs #ANCA #Vasculitis ... differential #diagnosis #algorithm ... #rheumatology
Hypereosinophilia and Hypereosinophilic Syndrome

 • Secondary Hypereosinophilic Syndrome
 • Clinically Relevant HES Variants
 • When to
Hypereosinophilic Syndrome • Clinically ... and Treatment Algorithm ... Syndrome #HES #Hematology ... #eosinophilia # ... #management #algorithm
2021 ACR/VF Guidelines for Management of Eosinophilic Granulomatosis with Polyangiitis (EGPA)

#EGPA #Eosinophilic #Granulomatosis #Polyangiitis #ACR2021 #Management
Guidelines for Management ... of Eosinophilic ... (EGPA) #EGPA #Eosinophilic ... #rheumatology # ... algorithm #vasculitis
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Polyangiitis (MPA) • Eosinophilic ... @MithuRheum #Vasculitis ... ACR2021 #Guidelines #algorithm ... #rheumatology
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Eosinophilic Granulomatosis ... (EGPA) - ANCA Vasculitis ... Management Algorithm ... #Management #Treatment ... #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
progressive) EGPA (Eosinophilic ... Polyangiitis): • Eosinophilia ... Mono Multiplex, Elevated ... Cogan syndrome: Ocular ... Differential #Diagnosis #Rheumatology
Giant Cell Arteritis (GCA) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Visual Symptoms/Loss or
Arteritis (GCA) - Vasculitis ... Management Algorithm ... Arteritis #GCA #Vasculitis ... #Management #Treatment ... #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... association • M > F Clinical ... Behcet syndrome (Clinical ... Syndrome #diagnosis #management ... signs #symptoms #rheumatology
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Related Disease Clinical ... phase reactants, eosinophilia ... No necrosis, No vasculitis ... Disease #diagnosis #management ... workup #treatment #rheumatology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
syndrome • Erythema elevatum ... Autoimmunity: • -MM/WM: Vasculitis ... Vasculitis) Autoantibodies ... Episodic angioedema+eosinophilia ... Paraproteinemias #Hematology