9 results
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... pathologically or clinically ... #diagnosis #algorithm ... #rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Granulomatosis with ... Vasculitis Management ... Algorithm - ACR ... #Vasculitis #Management ... #rheumatology
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Eosinophilic Granulomatosis ... Vasculitis Management ... Algorithm - ACR ... #Vasculitis #Management ... #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis Framework ... Differential Diagnosis ... Mono Multiplex, Elevated ... #Differential #Diagnosis ... #Rheumatology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Syndrome: • Clinical ... Labs/Diagnosis: ... cryoglobulins • Elevated ... DDX: • ANCA (Antineutrophil ... Cryoglobulins #diagnosis
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
) Suspect: Clinical ... Differential Diagnosis ... Malignancy (e.g. hematologic ... sediment, and elevated ... Erythematosus #Diagnosis
Autoimmune Hepatitis

Clinical Presentation
 - Highly variable clinical presentation, from subclinical disease to acute liver failure.
 -
Highly variable clinical ... IgG typically elevated ... : Auto-Nuclear ANA ... Hepatitis (eg Viral) Management ... #Management #Hepatology
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
• Serum IgG4 elevated ... specific) COMMON CLINICAL ... aortitis, mimics vasculitis ... breast, skin DIAGNOSIS ... #Management #Rheumatology
TAFRO

TAFRO syndrome was first described in 2010, standing for:
- Thrombocytopenia
- Anasarca
- Fever
- Reticulin fibrosis
- Organomegaly

TAFRO syndrome
Sjögren’s syndrome, ANCA-associated ... vasculitis - Infectious ... Histopathological Diagnoses ... Thrombocytopenia - Elevated ... #management #rheumatology