9 results
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
autoimmune disease ... and progressive fibrosis ... of Scleroderma (SSc ... : ILD (interstitial ... #rheumatology #
Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
SSc: systemic sclerosis ... lupus. ... ConnectiveTissueDiseases #ILD ... Comparison #Table #Pulmonary ... #Rheumatology #
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
ILD caused by inhalation ... : • Systemic sclerosis ... Polymyositis-dermatomyositis, Lupus ... fibrosis (IPF), ... #causes
Systemic Lupus Erythematosus - Summary
Antinuclear (ANA) - 95% - Initial screening test
Anti-dsDNA - 50%
 • Associated
Systemic Lupus Erythematosus ... - Summary Antinuclear ... activity Anti-Ro/SSA ... Treatment: • Mild ... diagnosis #rheumatology
Antinuclear Antibodies (ANA)
ANA or Anti-NucIear Antibody refers to antibodies against antigens in the nucleus → like
or scleroderma (SSc ... : Lupus (SLE), Systemic ... , Interstitial Pulmonary ... Fibrosis, Multiple ... ANA #patterns #rheumatology
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Causes of Interstitial ... Interstitial Pneumonia - fibrosis ... Rheumatoid Arthritis, Systemic ... Lupus and Scleroderma ... #ILD #Causes #Differential
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
SLE (Systemic Lupus ... Non-autoimmune rheumatologic ... • Prolidase deficiency ... CNS • Headache, mild ... #Diagnosis #Rheumatology
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
Anti-ENA - Rare (SSA ... Prognosis: Usually mild ... months to years) Systemic ... Evolution: Chronic disease ... comparison #table #rheumatology
Peripartum Cardiomyopathy - Summary
1. Definition
 • Towards the end of pregnancy to 5 months postpartum
Cardiomyopathy - Summary ... exclude other causes ... cardiomyopathy • Pulmonary ... LV thrombus, RV systolic ... Avoid ARBs • ICD