11 results
Cutaneous manifestations associated with myelodysplastic syndrome
 • Myeloid hemopathy with the most frequent skin lesions (20%)
Cutaneous manifestations ... manifestations (dermatomyositis ... leukocytoclastic vasculitis ... #differential #diagnosis ... #dermatology #oncology
Mechanic’s Hands in Dermatomyositis

Finally, mechanic’s hands which are common to Anti-synthetase syndrome and another type of
Anti-synthetase syndrome ... another type of DM ... of the distal finger ... #Dermatology #Clinical ... #Photo
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
Cutaneous manifestations ... chest (in a V-sign ... • Anti-MDA5 DM ... #rheumatology #dermatology ... #diagnosis
Dermatomyositis (DM) and Polymyositis (PM): Pathogenesis and clinical findings
Elevated Antinuclear Antibodies: Anti-Jo-1, Anti-OJ, Anti-Mi2, Anti-SRP, Anti-EJ,
Dermatomyositis ... (DM) and Polymyositis ... #PM #Diagnosis ... Pathophysiology #Signs ... #Symptoms #Vasculitis
Weakness - Differential Diagnosis Framework

Approach To Weakness:
 • Non-neuromuscular disorder (Cardiac, pulmonary etc)
 • CNS ->
- Differential Diagnosis ... polyneuropathy: DM ... Mononeuritis multiplex (DM ... Lack of UMN/LMN signs ... Muscle Biopsy: Dermatomyositis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... aphthous ulcers, cutaneous ... episcleritis as well as inner ... purpura: strong sign ... of cutaneous leukocytoclastic
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
Most common extra cutaneous ... Episcleritis Signs ... multiforme - Dermatomyositis ... Leukocytoclastic vasculitis ... #diagnosis #dermatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis Framework ... Differential Diagnosis ... purpura: Strong sign ... • Cogan syndrome ... episcleritis as well as inner
Cold Agglutinin Disease

3 Types of Cold Sensitive Antibodies:
  1. Cold Agglutinins (CAD)
  2. Donath-Landsteiner
Cryoglobulins (Vasculitic ... Cold Agglutinin Syndrome ... nose, ears, or fingers ... presentation) • Cutaneous ... hemolytic #anemia #hematology
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
DM with generalized ... in the neck Cutaneous ... to have typical DM ... chest (in a V-sign ... #rheumatology #dermatology