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Miller Fisher Syndrome (MFS) on Neurological Examination

Miller Fisher Syndrome (MFS)- a variant of Guillain Barre syndrome
Miller Fisher Syndrome ... Examination Miller Fisher ... Syndrome (MFS)- ... Guillain Barre syndrome ... #MFS #Miller #Fisher
Important Causes of Diplopia 
TIER 1-CRITICAL
Basilar artery thrombosis, Botulism, Basilar meningitis, Aneurysmn
TIER 2-EMERGENT:
Vertebral dissection, Myasthenia gravis,
, Orbital apex syndrome ... tumor, Miller-Fisher ... syndrome, Multiple
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
Guillain-Barre Syndrome ... death Miller Fisher ... Syndrome: • Opthaloplegia ... associated with Miller Fisher ... Guillain #Barre #Syndrome
Multiple Cranial Neuropathies - High Yield Differential Diagnosis
 • Intrinsic brainstem process
 • Compressive brainstem process
Carcinomatosis • Miller Fisher ... Syndrome variant-GBS
Rhombencephalitis
BACTERIAL
- Listeria (biphasic illness with bulbar dysfunction occurring later)
- Mycobacterium tuberculosis
- Pneumococcus
- Brucella
- Borrelia (Lyme Disease)
-
polychondritis - Sjogren's syndrome ... - Bickerstaff syndrome ... myasthenia, Miller-Fisher ... opsoclonus-myoclonus syndrome
NINDS Diagnostic Criteria for Guillain Barre Syndrome 
Features Required for Guillain-Barré Syndrome:
 • Progressive muscle weakness
Guillain Barre Syndrome ... Guillain-Barré Syndrome ... except in Miller Fisher ... syndrome-Bickerstaff ... Guillain #Barre #Syndrome
Differential diagnoses for the neuro-ophthalmologic finding of diplopia.
Neoplastic: 
 • Intraorbital meningioma 
 • Pituitary adenoma
GBS • Miller-Fisher ... syndrome • Orbital
Pancytopenia - Workup and Differential Diagnosis Algorithm
Consumption Disorders
 1. Autoimmune Mediated Pancytopenia
 2. Splenic Sequestration
Peripheral Destruction
HLH syndrome 5. ... Cytogenetics and FISH ... marrow failure syndrome
Myasthenia Gravis Overview

Myasthenia Gravis is an autoimmune disorder of the postsynaptic neuromuscular junction.  Ab to
thyroid, Sjogren syndrome ... “dropping head syndrome ... - Kearns-Sayre syndrome ... - Miller Fischer ... stimulation - Single fiber
Pancytopenia - Workup and Differential Diagnosis Algorithm
Consumption Disorders
 1. Autoimmune Mediated Pancytopenia
 2. Splenic Sequestration
Peripheral Destruction
HLH syndrome 5 ... Cytogenetics and FISH ... marrow failure syndrome