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Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... for Pulmonary Renal ... vasculitis, Behcet disease ... sclerosis • Anti-Glomerular ... Goodpasture's Disease
Membranoproliferative Glomerulonephritis (MPGN) AKA: Mesangiocapillary GN
 • Active Urine Sediment (dysmorphic RBC, RBC casts, +/- proteinuria)
formation along glomerular ... HBV, Sjogren's, rheumatoid ... (Dense deposit disease ... MPGN #nephrology #diagnosis ... #renal
Rheumatoid Arthritis - Signs and Symptoms
 • Ocular: Keratoconjunctivitis sicca, Episcleritis, Scleritis, Scleromalacia perforans
 • Pulmonary:
- Signs and Symptoms ... Parenchymal lung disease ... , Pleural disease ... , Airways disease ... #Symptoms #diagnosis
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Pulmonary Renal ... life-threatening diseases ... Inflammatory eye disease ... injury), Coags ... hypercellular glomeruli
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis - Skin, glomeruli ... disease, and ocular ... : - Kidneys: glomerular ... (Granulomatous disease ... diseases, such
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
diseases, such ... atherosclerotic disease ... most important diseases ... (GRANULOMATOUS DISEASE ... • Kidneys: Non-glomerular
Ankylosing Spondylitis: Extra-articular Manifestations
 • Ocular - Inflammation of the iris, the anterior part of the
Inflammatory Bowel Disease ... abnormalities • Renal ... amyloid proteins in glomeruli ... #diagnosis #signs ... #symptoms