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Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... Dyspnea, Fever, Hematuria ... for Pulmonary Renal ... sclerosis • Anti-Glomerular ... #Renal #Syndrome
Causes of Hematuria - Differential Diagnosis
Renal:
 - Glomerular - IgA Nephropathy, Thin basement membrane, Alport syndrome,
Renal: - Glomerular ... membrane, Alport syndrome ... , Other glomerulonephritis ... - Interstitial nephritis ... Medullary sponge kidney
Acute Kidney Injury - Classification
Prerenal:
 • Dehydration
 • Heart failure (a.k.a. cardiorenal syndrome)
 • Liver failure
- Small vessel vasculitis ... - TTP/HUS • Glomerular ... glomerulonephritis ... Acute interstitial nephritis ... #diagnosis #nephrology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
multiplex • Hematuria ... - Skin, glomeruli ... pulmonary disease ... : glomerular ischemia ... Kidneys -> glomerulonephritis
Hematuria - Differential Diagnosis Framework

Gross Hematuria: Red/Dark urine
 • 1ml blood/liter urine can induce color change
or dipstick) Glomerular ... • Causes of Glomerular ... • Signs of glomerular ... Suggestive of glomerular ... disease Renal
Rheumatoid Arthritis - Signs and Symptoms
 • Ocular: Keratoconjunctivitis sicca, Episcleritis, Scleritis, Scleromalacia perforans
 • Pulmonary:
Rheumatoid Arthritis ... vasculitis, Raynaud's ... Pericarditis • Renal ... #Rheumatoid #Arthritis ... #diagnosis #rheumatology
Membranoproliferative Glomerulonephritis (MPGN) AKA: Mesangiocapillary GN
 • Active Urine Sediment (dysmorphic RBC, RBC casts, +/- proteinuria)
formation along glomerular ... HBV, Sjogren's, rheumatoid ... arthritis, monoclonal ... (Dense deposit disease ... #renal
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Pulmonary Renal ... Renal Syndromes ... mononeuritis multiplex WORKUP ... hypercellular glomeruli ... #Renal #Syndromes
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
and renal abnormalities ... rheumatic diseases ... purpura: Strong sign ... : Non-glomerular ... pulmonary disease
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
Classification: ... Differential Diagnosis ... , rheumatoid arthritis ... proteinuria, hematuria ... APLA/LAC: • Renal