2191 results
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
presentation of the disease ... GPA causes disease ... Usually parallel the disease ... extravascular palisading granulomas ... rash #diagnosis #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Polyangiitis: - No Granulomas ... rhinosinusitis, + Granulomas ... • GPA: - +Granulomas ... (Granulomatous disease ... differential #diagnosis #rheumatology
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... vasculitis, No granuloma ... IgG4 #Related #Disease ... workup #treatment #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
atherosclerotic disease ... polyangiitis • No Granulomas ... rhinosinusitis • Granulomas ... Polyangiitis): • (-Granulomas ... Differential #Diagnosis #Rheumatology
Causes of Hypercalcemia due to increased Vitamin D levels
 • The BIG 3:
granulomatous diseases ... vasculitis, Crohn's disease ... pneumonia, Talc granuloma ... Silicone-induced granuloma ... Paraffin-associated granuloma
Diagnostic Schema for Hyperferritinemia

Pearl: Diseases associated with extreme elevations: 
1. HLH 
2. Still's disease 
3. Systemic
Hyperferritinemia Pearl: Diseases ... Still's disease ... Differential #Diagnosis #Hematology
Causes of Granulomatous Liver Diseases - Differential Diagnosis
Infections (Bacterial, Viral, Fungal, Parasitic)
Malignancy
Autoimmune
Drugs/Toxins
Others

#Granulomatous #Liver #hepatic #granulomas #Differential
Granulomatous Liver Diseases ... Liver #hepatic #granulomas
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
the presence of granulomas ... diagnosis #algorithm #rheumatology
Sarcoidosis 
Non-caseating granulomas (Composed of T-helper & inflammatory cells) 
Clinical:
 • Disease fatal in 10% of
Non-caseating granulomas ... Clinical: • Disease
Raynaud's Phenomenon on Physical Exam

#Raynauds #Syndrome #disease #phenomenon #clinical #video #physicalexam #fingers #hands #rheumatology
Raynauds #Syndrome #disease ... fingers #hands #rheumatology