12 results
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
pro-inflammatory cytokines ... , such as IL-1 and ... with leukopenia, anemia ... Histopathologic criteria ... #Diagnosis #Management
Aplastic Anemia - Overview

Who?
• M = F
• 3 peaks:	1) Childhood	2) 15-25 years	3) >60 years

What?
• Aplastic anemia
F • 3 peaks: 1) ... Constitutional Syndromes ... Clinical Presentation ... oncology #hematology #diagnosis ... #management
Renal Cell Carcinoma (RCC) - Diagnosis and Management Summary
Clinical features - Classic triad (flank pain, hematuria,
and Management ... Summary Clinical ... Anemia (common) ... Budd Chiari syndrome ... ), Recombinant cytokines
Acute Respiratory Distress Syndrome – ARDS: Clinical Cheat Sheet

An acute diffuse, inflammatory lung injury, leading to
– ARDS: Clinical ... Berlin criteria ... Acute onset over 1 ... week or less ● ... Summary #CheatSheet #Diagnosis
Sarcoidosis - Diagnosis and Management Summary
Epidemiology
1) High incidence in Scandinavian countries (11-24 cases per 100,000 individuals
Sarcoidosis - Diagnosis ... and Management ... Epithelioid cells → cytokines ... renal failure Clinical ... #Management #Signs
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
Epidemiology: • 1- ... - HIV, CMV, EBV ... Guillain-Barre Clinical ... main variants: (1) ... #diagnosis #management
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
• Affects 1:25,000 ... and 1:50,000 patients ... to 8 years Clinical ... autoimmune hemolytic anemia ... #management
KSHV Inflammatory Cytokine Syndrome (KICS)
Working Case Definition for KICS: Requires at least 2 clinical manifestations (from
Syndrome (KICS) ... together with each of criteria ... 2, 3, and 4. 1) ... abnormalities: Anemia ... #diagnosis #management
Hepatopulmonary Syndrome - Diagnosis and Management Summary
A defect in arterial oxygenation due to a gas exchange
Hepatopulmonary Syndrome ... diffusion-perfusion defect (Type 1) ... shunt (Type 2) Clinical ... Criteria: • Underlying ... #diagnosis #management
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
dysfunction. 1. ... Clinical Presentation ... - Cytopenias (anemia ... • Cytokine storm ... Diagnostic Criteria