36 results
Atrioventricular Septal Defect
aka AV canal defect aka endocardial cushion defect
 • Epidemiology and Associations
 • Embryology
• Epidemiology and ... Physical Exam • Pathophysiology ... Management • Long Term ... diagnosis #management #peds ... #pediatrics #cardiology
Behcet's Syndrome - Treatment
Ulcers:
 • Treatment: Topical steroids
 • Prevention: Colchicine
 • Azathioprine for refractory disease
Arthritis:
Behcet's Syndrome - Treatment ... Ulcers: • Treatment ... • Azathioprine and ... refractory lesions • Derm ... #pharmacology #rheumatology
Decompression Sickness - The physical examination revealed diffuse violaceous skin mottling over his trunk and arms
over his trunk and ... of the nausea and ... #Clinical #Derm ... #EM #Radiology # ... Pneumatosis #CT #NEJM
Plain radiography of the abdomen revealed calcification of both adrenal glands. A homozygous mutation in LIPA
acid lipase is critical ... liver, spleen, and ... #clincial #peds ... calcifications #infant #NEJM ... #Wolmans #radiology
CNS Manifestations of Systemic Lupus Erythematosus (SLE)

Clinical Manifestations: Demyelinating Syndrome, Headache, Movement disorders, Seizure disorders, Aseptic
Erythematosus (SLE) Clinical ... Disease, PRES Pathophysiology ... Puncture, EEG Treatment ... CNS #neurology #rheumatology ... diagnosis #management #treatment
TRALI vs TACO - Transfusion Reactions
TRALI:
 • Epidemiology: 0.1% of transfused patientsl
 • Risk factors: Critical
Risk factors: Critical ... blood donor • Pathophysiology ... : 33% • Treatment ... transfusion • Pathophysiology ... : No • Treatment
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Related Disease Clinical ... with response to treatment ... IgG4+ cells" Treatment ... supporting long-term ... #rheumatology
Congenital Long QT Syndrome: Illness Script

Who?
 - Kids or young adults, usually < 30
 - high
syncope/seizures and ... consider long term ... QT prolonging meds ... family history) Treatment ... Syndrome #Diagnosis #Cardiology
Tinea Capitis in a Newborn- A 3-week-old male newborn was brought to the pediatrician with three
lesions, which had ... after 1 week of treatment ... #clinical #photo ... #NEJM #tinea #capitis ... #ringworm #derm
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Lymphohistiocytosis (HLH) Pathophysiology ... accumulation of clinical ... Assessment • Clinical ... Unknown cause Treatment ... #summary #rheumatology