2003 results
Diagnostic algorithm for a child or adolescent with suspected pulmonary hypertension. CHD, congenital heart disease; CPET,
hypertension. ... hypertension; CXR ... hypertension; PVOD ... ; CLD, chronic lung ... #Hypertension #
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Pulmonary hypertension ... Pulmonary hypertension ... due to lung disease ... Interstitial lung ... Pulmonary hypertension
Causes of Pulmonary Hypertension - Differential Diagnosis Algorithm
Pulmonary Arterial Hypertension
 • Idiopathic
 • Associated with:
Causes of Pulmonary ... Hypertension - ... Diagnosis Algorithm Pulmonary ... • Valvular Lung ... • Interstitial Lung
Pulmonary Function Tests (PFTs) - Interpretation Algorithm
 • Normal
 • Pulmonary Hypertension, Anemia, Carboxyhemoglobinemia
 • Chest
Pulmonary Function ... • Normal • Pulmonary ... Hypertension, Anemia ... • Interstitial Lung ... Emphysematous COPD #Pulmonary
Right-Sided Heart Failure - Differential Diagnosis Algorithm
Cardiac Causes - Rule out Left-Sided Heart Failure (Most Common):
Valves • Pulmonary ... • Diffuse Lung ... • Chronic Lung ... Arterial Hypertension ... • Pulmonary
Multifocal Atrial Tachycardia (MAT)
• At least 3 different P wave morphologies: 
• Rate 100-180
• Irregular 
Etiology
Secondary to chronic lung ... • Hypoxia • Pulmonary ... hypertension
Causes of Hypoxemia- Differential Diagnosis Algorithm
Ventilation/perfusion Mismatch
 • Airway Disease (Asthma, COPD)
 • Vascular (PE*)
 •
• Interstitial lung ... disease • Pulmonary ... Arterial Hypertension ... Septal Defect Pulmonary ... Algorithm #Causes #Pulmonary
Sarcoidosis
Stage 1 - Bilateral LAD without involvement of lung parenchyma
Stage 2 - Bilateral LAD with involvement
involvement of lung ... involvement of lung ... 4 - Fibrosis Pulmonary ... chylothorax, and pulmonary ... hypertension are
Causes of Dyspnea - Differential Diagnosis Algorithm
Cardiac:
 • Dysrhythmia
 • Ischemia
 • Cardiomyopathy
 • Valvular disease
Pneumonia • Pulmonary ... • Interstitial lung ... Vasculature: • Pulmonary ... embolism • Pulmonary ... hypertension
Chronic Thromboembolic Pulmonary Hypertension (CTEPH) and Pulmonary Thromboendarterectomy
Chronic Thromboembolic Pulmonary Hypertension
Definition: mean pulmonary-artery pressure > 25mmHg
Hypertension (CTEPH ... ) and Pulmonary ... Hypertension Definition ... Ventilation-perfusion lung ... #Hypertension #