12 results
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Management of Hypocomplementemic ... Urticarial Vasculitis ... vasculitis 3) Hypocomplementemia ... TerrierBen #Hypocomplementemic ... Diagnosis #Management #Rheumatology
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology of Hypocomplementemic ... Urticarial Vasculitis ... TerrierBen #Hypocomplementemic ... #Urticarial #Vasculitis ... Pathophysiology #Rheumatology
Causes of Hypocomplementemia - CHAMPS Mnemonic
C - Cryoglobulinemia (85%), C3 glomerulopathy, cirrhosis
H - Heavy Chain deposition
Causes of Hypocomplementemia ... @AnnKumfer #Hypocomplementemia ... #differential #hematology
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
pseudotumor 4 phenotypes ... rheumatoid factor), ± hypocomplementemia ... diagnosis #management #phenotypes ... workup #treatment #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
often involved • Hypocomplementemic ... Urticarial Vasculitis ... Vasculitis): - Urticaria ... and hypocomplementemia ... cryoglobulinemia, urticarial
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Elevated AST ALT • Hypocomplementemia ... : Urticarial Vasculitis ... Vasculitis) • Hypocomplementemic ... Urticarial Vasculitis ... Differential #Diagnosis #Rheumatology
Reactive Skin Rash - Differential Diagnosis Algorithm
Reactive erythematous with various morphology
 • Urticaria - Firm /
Differential Diagnosis Algorithm ... morphology • Urticaria ... Reactive #SkinRash #dermatology ... Differential #Diagnosis #Algorithm
Pruritus - Primary Skin Lesion - Differential Diagnosis Algorithm
Macules / Papules / Plaques:
 • Xerosis (dry
Differential Diagnosis Algorithm ... Wheals/Hives: • Urticaria ... Pruritus #primary #dermatology ... Differential #Diagnosis #Algorithm
Hemolytic Anemia - Differential Diagnosis Algorithm
 • Sickle cells - Consider sickle cell disease (diverse genotypes):
Differential Diagnosis Algorithm ... disease (diverse genotypes ... Differential #Diagnosis #Algorithm ... #workup #hematology
Dematoses in Pregnancy - Specific Skin Conditions
Non-Pruritic
 • Pustular psoriasis of pregnancy
 • Impetigo Herpetiformis
Pruritic -
gestationis • Pruritic urticarial ... pregnancy #rash #dermatology ... Differential #Diagnosis #Algorithm