15 results
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Diagnosis and Management ... of Hypocomplementemic ... 3) Hypocomplementemia ... 2nd-line therapy - GCs ... TerrierBen #Hypocomplementemic
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology of Hypocomplementemic ... Urticarial Vasculitis ... Complex Formation - Complement ... Formation -> Vasculitis ... TerrierBen #Hypocomplementemic
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
> PR3 60% • GPA ... often involved • Hypocomplementemic ... Urticaria and hypocomplementemia ... and branches • GCA ... against MPO • Complement
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Cell Arteritis (GCA ... Sources: GCA ... @MithuRheum #Vasculitis ... ACR2021 #Guidelines #algorithm
Giant Cell Arteritis (GCA) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Visual Symptoms/Loss or
Cell Arteritis (GCA ... ) - Vasculitis Management ... Algorithm - ACR ... GiantCell #Arteritis #GCA ... #Vasculitis #Management
2021 ACR/VF Guidelines for Management of Giant Cell Arteritis (GCA)

#GiantCell #Arteritis #GCA #ACR2021 #Management #rheumatology #algorithm
Guidelines for Management ... Cell Arteritis (GCA ... #ACR2021 #Management ... #rheumatology #algorithm ... #vasculitis
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Elevated ESR and CRP GCA ... develop in pts with GCA ... MPO > PR3 60/ GPA ... Elevated AST ALT • Hypocomplementemia ... ) • Hypocomplementemic
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (MPA) - ANCA Vasculitis ... Management Algorithm ... Polyangiitis #MPA #ANCA #Vasculitis ... #Management #Treatment ... ACR2021 #Guidelines #algorithm
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
rheumatoid factor), ± hypocomplementemia ... No necrosis, No vasculitis ... maintenance with GCs ... GC-dependency ... Disease #diagnosis #management
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
staining): • Low Complement ... Idiopathic • Normal Complement ... ANCA (C-ANCA): GPA ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm