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Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
lung diseases ... I-JIP: usual interstitial ... AIP: acute interstitial ... PSS: Sjogren syndrome ... #Comparison #Table
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
Interstitial Lung ... lung disease (RB-ILD ... Churg Strauss syndrome ... #differential # ... pulmonary #causes
Differential diagnosis on HRCT
Most of our knowledge about imaging findings in interstitial lung disease comes from
Differential diagnosis ... low attenuation (table ... in many cases UIP ... Diagnosis #Radiology #Pulmonary ... #Pattern #Differential
The idiopathic interstitial pneumonias (IIPs) comprise a heterogenous group of disorders. 
They represent fundamental responses of
listed in the table ... have specific patterns ... Diagnosis #Radiology #Pulmonary ... #CTChest #Idiopathic ... IdiopathicInterstitialPneumonia #ILD
The fourth pattern includes abnormalities that result in decreased lung attenuation or air-filled lesions.
These include:
- Emphysema
-
cysts (LAM, LIP ... Diagnosis #Radiology #Pulmonary ... #CTChest #LowAttenuation ... #Differential # ... Diagram #Comparison
Ground-glass opacity
Ground-glass opacity (GGO) represents:
- Filling of the alveolar spaces with pus, edema, hemorrhage, inflammation or
lung disease (i.e ... in ground glass pattern ... predominance: UIP ... #CTChest #GGO # ... #GroundGlass #Differential
Figure 3 HRCT-LUS correlation in normal lung, pulmonary congestion, rheumatoid lung disease, idiopathic pulmonary fibrosis.
Notes: (A)
due to alveolar syndrome ... artifact); (G) UIP ... pattern with subpleural ... #Correlation #Table ... #ILD #Findings
On the left some diseases with a nodular pattern.
1. Hypersensitivity pneumonitis: ill defined centrilobular nodules.
2. Miliary
with a nodular pattern ... Diagnosis #Radiology #Pulmonary ... #CTChest #Nodular ... #Differential # ... Comparison #Table
Causes of Chronic Dyspnea - Differential Diagnosis Algorithm
Pericardial
 • Effusion
 • Cardiac Tamponade*
 • Constriction
Myocardial
 •
Chronic Dyspnea - Differential ... Artery Disease • Stable ... Acute Coronary Syndrome ... Interstitium ... • ILD • CHF
Septal thickening
Thickening of the lung interstitium by fluid, fibrous tissue, or infiltration by cells results in
Thickening of the lung ... cells results in a pattern ... lung disease, it ... diagnosis (Table ... pulmonary edema