75 results
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
accumulation of clinical ... Assessment • Clinical ... Purtilo (XLP) Acquired ... • Autoimmune diseases ... #summary #rheumatology
Classification of Diabetes Insipidus

Central or neurogenic diabetes insipidus:
 - Congenital - Structural malformations affecting the hypothalamus
or metastases, Infection ... AQP-2 gene - Acquired ... hypercalcemia), Sickle cell ... Treatment is aimed ... Types #Nephrology #Diagnosis
Chronic Lymphocytic Leukemia - Summary

Cancer affecting lymphocytes/Mature B cell neoplasm
 • Lymphocytes accumulate in large numbers
Lymphocytic Leukemia - Summary ... Orange or Hep C Clinical ... weeks without infection ... cells can indicate disease ... microglobulin Treatment
Shock - Diagnosis and Management Summary
 • Hypotension: SBP<90, SBP drop >40, MAP<65 (Normotension, HTN possible
Shock - Diagnosis ... and Management Summary ... support - Call ... Tamponade - Pulmonary ... #treatment #workup
Mycoses

HISTOPLASMOSIS
• Inhalation of conidia → Yeast → travel to lymph nodes → spread in body
• Bird
has five major clinical ... extrapulmonary disease ... fungal stain of clinical ... becomes a yeast cell ... fever • Septic shock
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
to impaired B-cell ... late adulthood • Diagnosis ... to 8 years Clinical ... severe community-acquired ... conditions Diagnosis
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
life Causes and clinical ... Infections 2. ... , Hypotension, shock ... Disorientation, vertigo Diagnostic ... Cold #Urticaria #diagnosis
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Clinical triad ... Differential Diaqnoses ... : • Infectious ... hepatitis • Pulmonary ... #treatment #rheumatology
Blastomycosis (Blastomyces): Gilchrist’s disease, Chicago disease - Summary Sheet
 • Morphology
 • Geography, Reservoir and Mode
- Summary Sheet ... inoculation • Clinical ... resembles community-acquired ... #Blastomyces #diagnosis ... #management #summary
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... - HIV infection ... pulmonary disease ... Langerhans cell ... Classification #Diagnosis