44 results
Summary of Coagulation Deficiencies
Inherited:
 • Hemophilia A - Deficiency of Factor VIII
 • Hemophilia B -
of Factor IX Acquired ... Acute DIC - Septic shock ... Deficiencies #Summary #table ... #comparison #diagnosis ... #hematology #deficiency
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
the secondary or acquired ... highly inflammatory disease ... Activation #Syndrome #Diagnosis ... #Management #Hematology ... #Rheumatology
Nail Findings & Associated Conditions
Change in color, texture, or shape can be harmless, but may suggest
texture, or shape can ... an underlying systemic ... disease ... #differential #diagnosis ... #table #lines
Nail Findings & Associated Conditions
Change in color, texture, or shape can be harmless, but may suggest
texture, or shape can ... an underlying systemic ... disease ... #differential #diagnosis ... #table #lines
Systemic Lupus Erythematosus (SLE) - Diagnosis and Management Summary
 • Epidemiology: 10-180/100,000, Typically Age 20-40, F:M
Systemic Lupus Erythematosus ... (SLE) - Diagnosis ... Manifestations: - CRP ... Evolution: Chronic disease ... #rheumatology
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
-> 40 years • Can ... severe community-acquired ... hemolytic anemia) • Systemic ... hypogammaglobulinemia #immunology #hematology ... #diagnosis #management
Pulmonary Arterial Catheterization – Use and Interpretation:
-Pulmonary arterial catheterization (PAC) has never been shown to improve
or the type of shock ... obtained by PAC can ... acute valvular disease ... cardiac index) -systemic ... #Differential #Table
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• Heavy Chain disease ... angioedema • vWD • acquired ... Sneddon-Wilkinson disease ... Paraproteinemias #Hematology ... #Differential #Diagnosis
Adult-Onset Still's Disease (AOSD)
Rare inflammatory disorder of unknown etiology, difficult to diagnose because of heterogenous presentation.
Adult-Onset Still's Disease ... episode (30%) Systemic ... AOSD: high fever, CRP ... #AOSD #rheumatology ... #diagnosis #management
Subglottic stenoses (SGS) during systemic diseases
Subglottic stenosis (SGS) = congenital (children) or acquired (adult) characterized by
stenoses (SGS) during systemic ... (children) or acquired ... ++ • PET-CT Acquired ... #diagnosis #causes ... #rheumatology