17 results
Jaundice and Kayser-Fleischer Rings in Wilson's Disease

#Jaundice #Kayser #Fleischer #Rings #Wilsons #Disease #clinical #video #ocular #physicalexam
Rings in Wilson's ... Disease #Jaundice ... #Kayser #Fleischer ... #Rings #Wilsons ... video #ocular #physicalexam
Kayser-Fleischer Rings of Wilson's Disease seen on Physical Exam

#Kayser #Fleischer #Rings #PhysicalExam #clinical #video #ophthalmology #Wilsons
Kayser-Fleischer ... Rings of Wilson's ... Disease seen on ... #Rings #PhysicalExam ... #disease #copper
Clinical Examination for Liver and Biliary Diseases
1) Hands: Clubbing, Dupuytren's contracture, Leuconychia, Bruising, Flapping tremor (hepatic
cholestasis, Kayser-Fleischer ... rings in Wilson's ... Edema #biliary #physicalexam ... #cirrhosis #liver ... #diagnosis
Common Etiologies of Cirrhosis

Inflammation

 - Hepatitis B (15 percent)

 - Hepatitis C (47 percent)

 - Schistosomiasis
Etiologies of Cirrhosis ... Primary biliary cirrhosis ... - Wilson disease ... Venoocclusive disease ... 14 percent) #Diagnosis
Kayser-Fleisher´s ring (anillo de Kayser- Fleisher)
ring around the cornea .Copper deposit in  Desemet membrane (Wilson
Kayser-Fleisher´ ... anillo de Kayser- Fleisher ... Desemet membrane (Wilson ... disease) #PhysicalExam ... #Wilson #Eye #ring
Elevated Liver Enzymes - Differential Diagnosis Algorithm
Severe ALT > 15x ULN
 • Viral
 • Drugs/Toxins
 •
- Differential Diagnosis ... Autoimmune • Wilson's ... • Cholestatic disease ... Infiltrative • Cirrhosis ... #Differential #Diagnosis
Diagnostic Scoring System for Wilson's Disease
 - Kayser-Fleischer rings (2 points)
 - Neurological symptoms (2 points)
Diagnostic Scoring ... System for Wilson's ... Disease - Kayser-Fleischer ... very unlikely #Wilsons ... #Disease #Scoring
Hepatomegaly - Differential Diagnosis Algorithm
Malignant
 • Primary Carcinoma
 • Metastases
 • Lymphoma
 • Leukemia
 • Polycythemia
- Differential Diagnosis ... Hemochromatosis • Wilson's ... Disease • Amyloidosis ... Primary Biliary Cirrhosis ... #Differential #Diagnosis
Nail Disorders secondary to Systemic Diseases
Nail Fold Abnormality
 • SLE
 • Scleroderma
 • Dermatomyositis
Koilonychia - Spoon-shaped
secondary to Systemic Diseases ... Medications • Wilson's ... disease • Silver ... discoloration) • Liver cirrhosis ... #Differential #Diagnosis
Primary Biliary Cirrhosis (PBC) - Summary

PBC Epidemiology:
 • Female:Male 9:1
 • Common European descent
 • Age:
Primary Biliary Cirrhosis ... Pathophysiology: • T lymphocyte ... cholestasis → Cirrhosis ... but elevated as disease ... , IgG4 related disease