9 results
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Differential Diaqnoses ... abnormalities • Muscular ... Stills #Disease #diagnosis ... #management #treatment ... #rheumatology
Hepatopulmonary Syndrome - Diagnosis and Management Summary
A defect in arterial oxygenation due to a gas exchange
intrapulmonary vascular ... Intra-pulmonary vascular ... ) on room air Treatment ... #management #treatment ... #hepatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
disease (panuveitis, retinal ... and diplopia) • Vascular ... Arthritis, AS Treatment ... #management #signs ... #symptoms #rheumatology
Differentiation Syndrome in APML
Epidemiology:
 • Incidence: common in APL (2-48% depending on the study)
 • Triggers:
Triggers: ATRA treatment ... Cathepsin G release → vascular ... opacities • Diagnosis ... Renal Failure Treatment ... #management #hematology
Portopulmonary Hypertension
Presence of pulmonary arterial hypertension in a patient with portal hypertension
No other obvious causes (chronic
for definitive diagnosis ... Diagnostic criteria ... pressure < 15mmHg TREATMENT ... vasodilation and reduced vascular ... #management #hepatology
Intermittent Bilateral Exophthalmos (Alternating Exophthalmos and Enophthalmos) on Physical Exam

Observing this patient in silence for a
Patient underwent a diagnostic ... Treatments are aimed ... inflammatory, vascular ... Commonly, vascular ... Bilateral #clinical #video
Adult Onset Still's Disease
Systemic inflammation with urticarial rash.
Rash: 
 • Nonpruritic, evanescent (correlates with time of
A nonpruritic macular ... Treatment - Mild ... : NSAIDS Treatment ... #rheumatology # ... management
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
• No effective treatment ... IVIg) • Limit vascular ... leak #syndrome #diagnosis ... #management #timeline ... #treatment #rheumatology
TAFRO

TAFRO syndrome was first described in 2010, standing for:
- Thrombocytopenia
- Anasarca
- Fever
- Reticulin fibrosis
- Organomegaly

TAFRO syndrome
along with (VEGF) vascular ... Histopathological Diagnoses ... Hypoalbuminemia Treatment ... agonists #TAFRO #diagnosis ... #management #rheumatology