7 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... skin injury) • Neurologic ... syndrome (Clinical ... inhibitors • Uveitis- Ophthalmology ... #rheumatology #
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
scalp tenderness, jaw ... • Progressive symptoms ... tract, and often causes ... vasculitis • Behcet ... Differential #Diagnosis #Rheumatology
Spinal Cord Disorders - Differential Diagnosis Framework

Spinal cord neurological lesion:
Clinical findings:
 • Symptoms and signs below
neurological lesion: Clinical ... Non-compressive Spinal Cord Causes ... - Sarcoidosis, Behcet ... disease - SLE ... MCTD, Sjogren syndrome
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
with systemic, neurologic ... Diagnosis = clinical ... them, but urgent rheumatology ... required +/- prompt ophthalmology ... Temporal #Signs #Symptoms
Polymyalgia Rheumatica (PMR) Diagnosis and Management Summary

WHAT?
 • Polymyalgia rheumatica (PMR) is a common systemic inflammatory
of unknown cause ... tenosynovitis of the neck ... CLINICAL: • Physical ... visual changes, and jaw ... Diagnosis #Management #Rheumatology
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
ethnicities Symptoms ... the most common clinical ... + Nonspecific symptoms ... Sarcoidosis • Behcet ... Polychondritis #rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
caused by uncontrolled ... ▪ Autoimmune diseases ... Clinical Presentation ... Common Signs and Symptoms ... Emerging therapies: JAK