35 results
ANCA Vasculitis - GPA, MPA, Eosinophilic GPA

doi:10.1038/s41572-020-0204-y

#ANCA #Vasculitis #GPA #MPA #Eosinophilic #rheumatology #diagnosis #comparison #table
ANCA Vasculitis ... s41572-020-0204-y #ANCA ... #Vasculitis #GPA ... #Eosinophilic #rheumatology ... #diagnosis #comparison
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential ... Vasculitis: + MPO-ANCA ... ear disease Differential ... differential #diagnosis ... #rheumatology #
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Pauci-immune mediated (Negative ... (C-ANCA): GPA > ... Glomerulonephritis #Vasculitis ... #differential # ... diagnosis #algorithm #rheumatology
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
symptomatology Differential ... vasculitis (Eosinophilic ... polyangiitis) - ANCA-negative ... vasculitis, Behcet ... Renal #Syndrome #differential
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
the Skin - Differential ... • ANCA Associated ... #skin #dermatology ... #rheumatology # ... differential #diagnosis
Frequency of ANCA Positivity in Different Conditions
ANCA-Associated Vasculitis
 • GPA - PR3-ANCA 75%, MPO-ANCA 20%, 5%
5% ANCA negative ... , 10% ANCA negative ... , 50% ANCA negative ... ANCA negative ... PR3 #diagnosis #rheumatology
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... StanfordChiefs #ANCA ... #Vasculitis #differential ... diagnosis #algorithm #rheumatology
Diagnosis and management of Polyarteritis Nodosa (PAN)

Chapel Hill 2012 definition: 
Necrotizing vasculitis ofmedium or small arteries
Necrotizing vasculitis ... glomerulonephritis or vasculitis ... associated with ANCA ... PolyarteritisNodosa #Rheumatology ... #Differential
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (MPA) - ANCA ... Vasculitis Management ... Polyangiitis #MPA #ANCA ... #Vasculitis #Management ... #Treatment #ACR2021
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
Vasculitis - Break ... by large vessel vasculitis ... basement membrane; ANCA ... #Diagnosis #Rheumatology ... #Differential #