19 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... vasculitis - Skin ... Wide variety of skin ... : Ocular Behcet's ... #Syndrome #disease
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome ... ulceration • Ocular ... response to local skin ... injury) • Neurologic ... #management #signs
Behcet's Syndrome - Treatment
Ulcers:
 • Treatment: Topical steroids
 • Prevention: Colchicine
 • Azathioprine for refractory disease
Arthritis:
Behcet's Syndrome ... Skin manifestations ... refractory lesions Ocular ... #disease #Syndrome ... #Treatment #management
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
IgM deposits • Nodular ... Vasculitis: • Behcet ... Disease • Cogan ... syndrome #Cutaneous ... #dermatology #rheumatology
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
- SLE Neurologic ... Amyloidosis • Chorea ... vulvar ulcers - Behçet's ... ulcers - SLE, Behçet's ... Scleroderma Thickened skin
Ptosis - Differential Diagnosis Framework

Ptosis (Greek- to fall) Drooping of the upper eyelid that usually results
Neurogenic Ptosis - Neurologic ... disease affecting ... nerve palsy • Horner ... Redundant eyelid skin ... #Ptosis #neurology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
strength & enzymes normal ... , neurologic, and ... cognitive impairment, neurologic ... vasculitis • Behcet ... syndrome: Recurrent
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
, and ocular inflammation ... VASCULITIS: • Behçet ... Syndrome: - Recurrent ... oral and/or genital ... • Cogan Syndrome
Drug Reaction with Eosinophilia and Systemic Symptoms (DRESS)
Definition: 
 • Severe adverse drug reaction, characterized by
Skin involvement ... Oral/IV Glucocorticoids ... SinaiBmoreIMRes #DRESS #Syndrome ... #dermatology #diagnosis ... #management
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• Heavy Chain disease ... Alpha & Mu) Skin ... et diutinum Neurologic ... thrombosis+Pulm HTN+skin ... Cryoglobulinemic, Hypo/normo-complementemic