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Thrombotic Microangiopathies In Systemic Lupus Erythematosus

Dr. Laurent ARNAUD @Lupusreference

#TMAs #Thrombotic #Microangiopathies #Systemic #Lupus #Erythematosus #SLE #hematology
Lupusreference #TMAs ... Erythematosus #SLE #hematology ... #rheumatology # ... differential #diagnosis ... #causes
Hyperthermia Syndromes Comparison
Serotonin Syndrome - NMS - Malignant Hyperthermia - Malignant Catatonia
Cause - Onset - Vitals
Hyperthermia Syndromes ... Comparison Serotonin Syndrome ... Malignant Catatonia Cause ... Mental Status - Treatment ... #Comparison #diagnosis
Proposed Treatment Algorithm for MAS / HLH

#MAS #HLH #Hemophagocytic #Lymphohistiocytosis #Management #Treatment #Algorithm #Hematology
Proposed Treatment ... Algorithm for MAS ... / HLH #MAS # ... Lymphohistiocytosis #Management #Treatment ... #Algorithm #Hematology
Opsoclonus-Myoclonus Ataxia Syndrome (OMAS) -Dancing eyes - dancing feet syndrome
 • Opsoclonus: ocular spontaneous, arrhythmic, conjugate
Opsoclonus-Myoclonus Ataxia Syndrome ... (OMAS) -Dancing ... - dancing feet syndrome ... involuntary movements caused ... FatimahDandan #OMAS
Myelodysplastic Syndrome (MD) - Diagnosis and Management Summary
myelo (marrow) -dys- (abnormal) -plastic (shape) = funny-shaped cells
Myelodysplastic Syndrome ... old, ~10,000 new cases ... only curative treatment ... #Management #treatment ... #hematology #oncology
Hypereosinophilia and Hypereosinophilic Syndrome

 • Secondary Hypereosinophilic Syndrome
 • Clinically Relevant HES Variants
 • When to
Hypereosinophilic Syndrome ... disorders • Diagnosis ... and Treatment Algorithm ... #HES #Hematology ... #eosinophils #diagnosis
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Macrophage Activation Syndrome ... (MAS) Classified ... Treatment: • Corticosteroids ... #Diagnosis #Management ... #Hematology #Rheumatology
Thrombotic Microangiopathy - TMAs
1. Not all MAHAs are due to TMAs but (almost) all TMAs cause
Microangiopathy - TMAs ... MAHAs are due to TMAs ... but (almost) all TMAs ... cause MAHA. 2 ... #hematology #diagnosis
Common Raynaud's Mimickers
 - Acrocyanosis
 - Chill blains (pernio)
 - Erythromelalgia
 - Frostbite
 - Achenbach's Syndrome

Dr.
- Achenbach's Syndrome ... #Differential #Diagnosis ... #Causes #Mimics ... #rheumatology #
Chest pain, good story, but nonspecific ECG? Do a bedside echo: regional WMAs support your case
echo: regional WMAs ... support your case ... UltrasoundJelly #Clinical #Diagnosis ... Echocardiogram #WMAs