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Inherited Non-hemolytic Disorders of Hyperbilirubinemia 

== Disorders of Conjugation ==
Gilbert Syndrome:
 • 5-10% of the population
hyperbilirubinemia ... hyperbilirubinemia ... rarely results in kernicterus ... predominantly a mixed conjugated ... hyperbilirubinemia
Classification of Jaundice
Unconjugated hyperbilirubinemia (predominantly indirect bilirubin)
 • Increased bilirubin production (eg, hemolytic anemias, hemolytic reactions,
hyperbilirubinemia ... posthepatitis hyperbilirubinemia ... drug reactions) Conjugated ... hyperbilirubinemia ... conjugates (eg,
Approach to Conjugated Hyperbilirubinemia - Differential Diagnosis Algorithm

1. Definition: T.bili elevation + >20% conjugated
2. Obtain RUQ
Approach to Conjugated ... Hyperbilirubinemia ... elevation + >20% conjugated ... #Hyperbilirubinemia ... #direct #bilirubin
Inherited forms of Hyperbilirubinemia
Major pathways involved in bilirubin production, conjugation, and excretion. Notes: Both the UB
Inherited forms of Hyperbilirubinemia ... pathways involved in bilirubin ... bilirubin into ... Decreased MRP2 - Conjugated ... Inherited #forms #Hyperbilirubinemia