13 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... Uveitis or retinal vasculitis ... Clinical Features: • Painful ... uveitis, retinal vasculitis ... Diagnosis #criteria #rheumatology
Aortitis - Differential Diagnosis Framework
Non-Infectious Aortitis:
 • Vasculitides: Giant Cell Arteritis (GCA), Takayasu's arteritis, Cogan's Syndrome,
: • Vasculitides ... polychondritis, Behcet's ... ANCA associated vasculitis ... Arthritis (RA), Systemic ... Differential #Diagnosis #rheumatology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... central nervous system ... disease - systemic ... syndrome - Behcet ... #Diagnosis #Rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: • Behçet Syndrome ... central nervous system ... claudication, aortitis ... differential #diagnosis #rheumatology ... #classification
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome ... Systemic disease ... , small-vessel vasculitis ... aphthous ulcerations (painful ... signs #symptoms #rheumatology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
activate the immune system ... disorder (e.g. systemic ... diagnosis #types #classification ... #rheumatology # ... vasculitis
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis: • Systemic ... Presentation: Systemic ... Central Nervous System ... • Behcet syndrome ... Differential #Diagnosis #Rheumatology
Genital Ulcers - Atypical causes of genital ulcers that can be difficult to diagnose & manage.
chancre Can be painful ... like cancer but painful ... juvenile gangrenous vasculitis ... topical products - Behcet's ... accompanying GI and other systemic
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
neuropathy) • Systemic ... Organomegaly+↑RBC/plt ... Autoimmunity: • -MM/WM: Vasculitis ... Hypergammaglobulinemic macular Vasculitis ... Paraproteinemias #Hematology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... processes: • Systemic ... sensitivity • Painful ... reticularis • Painful ... Cryofibrinogenemia #diagnosis #rheumatology